Hemifacial hypertrophy abbreviated as (HFH) is rare congenital disease characterized by unilateral enlargement of the head and teeth. It is classified as true. Depending on involvement of soft tissues, teeth, and bones, he further classified hemifacial hypertrophy into (a) true hemifacial hypertrophy and. Two cases of congenital hemifacial hypertrophy are described. To our knowledge , this is the first report of this syndrome in a black African population. Possible.
|Published (Last):||5 July 2012|
|PDF File Size:||3.73 Mb|
|ePub File Size:||8.3 Mb|
|Price:||Free* [*Free Regsitration Required]|
OPG view showed that the mandible was unilaterally enlarged with the body of mandible being longer on the right side with an enlarged right condyle resulting in mandibular deviation to the left [ Figure 5 ].
Congenital hemifacial hyperplasia
Log in Sign up. Our case is consistent with the previous findings. Oral mucosa — Lining of mouth. American Journal of Neuroradiology. The left and right sides were almost equally affected. Till date, previous literature survey indicated no evidence of malignant transformation. These clinical conditions can be clearly differentiated from CHH based on specific radiographs and laboratory and clinical findings that supplemented our case diagnosis [ 20 ].
Diffuse enlargement of the right side of face beginning abruptly at the midline and deviation of nose, mouth and chin toward the nypertrophy side. Treatment modalities The treatment modalities extend from subtle soft tissue contouring to extensive surgeries to correct the underlying bony defect and reshape the overlying soft tissues. Case Reports in Dentistry. Hemifacial hyperplasia is generally associated with good prognosis.
No other physical abnormality was noted. Case Presentation A thirty-nine-year-old male patient reported to the Department of Oral Medicine and Radiology with a chief complaint of asymptomatic swelling in his right cheek region since birth.
Basal cell adenoma Canalicular adenoma Ductal papilloma Monomorphic adenoma Myoepithelioma Oncocytoma Papillary cystadenoma lymphomatosum Pleomorphic adenoma Sebaceous adenoma Malignant: Occasionally, a gross asymmetry easily perceptible to the eye may occur which progresses slowly but steadily and exhibits asymmetric development.
According to Rowe, the size and shape of the tooth crown and root size, as well as rate of development, are usually abnormal jemifacial the teeth are affected [ 3 hemidacial.
Congenital hemifacial hyperplasia
Author information Copyright and License information Disclaimer. Phosphatidylcholine preparations have been used internationally for localized reduction of subcutaneous fat deposits.
National Center for Biotechnology InformationU. Familial facial asymmetry autosomal dominant hemihypertrophy? If the critical concentration is not reached, the unstable cell membrane forms gaps or pores, allowing efflux hypertropy some of the cytoplasmic contents. Bednar’s aphthae Cleft palate High-arched palate Palatal cysts of the newborn Inflammatory papillary hyperplasia Stomatitis nicotina Torus palatinus.
However, the patients frequently required blood transfusions due to blood loss. The computed tomography showed uniform bony enlargement of the left half of the face including the frontal bone [ Figure 4 ]. The etiology of congenital hemifacial hypertrophy and one case report. Nose and chin were deviated with an observable arc shaped facial midlines nasion-gnathion. It was clear that there was a unilateral enhancement of development on this side.
An integrated multidisciplinary approach in the field of dentistry is essential in providing an asymptomatic treatment. Periodontium gingivaperiodontal ligamentcementumalveolus — Gums and tooth-supporting structures. Treatment ideally is not indicated for Congenital Hemifacial Hyperplasia CHH unless cosmetic considerations are involved.
It was also interesting to note that the premolars were the most enlarged among the teeth; however, the second molars which develop around the same period are not. The growth of the neural tube follows a cephalocaudal gradient of growth and it reasonable to expect that some tube segments are more involved than others. Children with idiopathic hemihypertrophy and Beckwith-Wiedemann syndrome have different constitutional epigenotypes associated with Wilms tumor.
The treatment modalities extend from subtle soft tissue contouring to extensive surgeries to correct the underlying bony defect and reshape the overlying soft tissues.
Clinical and imaging findings of true hemifacial hyperplasia. There was no evidence of regional lymphadenopathy. Views Read Edit View history.
Tumescent technique for local anesthesia improves safety in large-volume liposuction. Hemifacial hypeertrophy is also newly proposed and described as a separate entity in which there is predominantly hyperplasia of the facial musculature. Tumescent liposuction in the treatment of partial hemifacial hypertrophy.
Detailed coronal dimensions of the teeth were measured on the casts with vernier calipers, which revealed major variations in size between the teeth of the affected side compared to the uninvolved hypertdophy. Midline shift and altered occlusion with deviated occlusal plane are noticed. Several instances of male-to-male transmission were observed.
Report of two cases. Asymmetry in CHH is usually evident at birth and accentuated with age, especially at puberty. Clinical and imaging findings of true hemifacial hyperplasia. Hemifacial hypertrophy can cause a wide spectrum of defects or may involve only muscle or bone.